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What Are The Options To Treat Idiopathic Pulmonary Arterial Hypertension

May 30, 2023 | Blog

Has your pulmonologist confused you with the diagnosis of IPAH – Idiopathic Pulmonary Arterial Hypertension? It is time to let go of the confusion; stay with us till the end to learn about IPAH and its treatment.

What Is IPAH?

(IPAH) or Idiopathic Pulmonary Arterial Hypertension is a lung disorder characterized by high BP – blood pressure in the pulmonary arteries. The term idiopathic signifies that the cause is unknown.

This condition adds strain to the heart and leads to dangerous and complicated heart and lung complications. It is crucial to have an early diagnosis to better the survival chances and initiate appropriate treatment.

Unfortunately, there is no cure for IPAH yet; however, there are various medications and procedures that can help slow down its progression and enhance the quality of life.


IPAH symptoms are different for everyone, and the signs are more dependent on the stage of the disorder. When it is the early stages, you may not notice visible symptoms, making it challenging to detect during a routine check-up.

However, as the condition gets worse, the following symptoms may appear:

  • Tiredness
  • Shortness of breath
  • Fainting
  • Dizziness
  • Rapid pulse
  • Chest pain
  • Heart palpitations
  • Swelling of lower extremities

Idiopathic Pulmonary Arterial Hypertension Treatment Available

Even though doctors have not yet found a cure for IPAH yet, still, there are various approaches that aim to help with disease progression and provide relief from symptoms.

Intravenous/Subcutaneous Treatments

These treatments use medications administered directly into the bloodstream or beneath the skin to open up blood vessels, relieving chest pain and shortness of breath.

Oral Medications

Various oral medicinal drugs are available in the market for IPAH. Endothelin Receptor Antagonists (ERAs) are those medicines that help prevent blood vessel constriction, allowing patients to engage in physical activities.

On the other hand, Phosphodiesterase Inhibitors (PDE 5 Inhibitors) relax the lungs and dilate blood vessels.

Moreover, Prostacyclin Analogues, Selective IP Receptor Agonists, and Soluble Guanylate Cyclase (sGC) Stimulators promote the relaxation of blood vessels in the lungs.

Inhaled Treatments

Inhaled treatments, such as prostacyclin, are supposed to target shortness of breath. These therapies provide adjunctive support alongside regular medication.

Diuretics may be prescribed to treat fluid retention and swelling. Anticoagulants help prevent blood clot formation, while some patients may require portable oxygen tanks.

In severe cases, a heart-lung, single-lung, or double-lung transplant may be recommended. Pulmonary rehabilitation and regular exercise are highly encouraged to improve breathing and enhance the quality of life.

Closing Note

Get in touch with a lung doctor in Houston to treat your condition for long-term relief. Connect with the pulmonologist from Pulmonary Medical Consultant right away! We are located at 27721 State Highway 249, Suite 300, Tomball, TX 77375. Dial (281) 357-1300 to connect with us right away.


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